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Management of immune suppression in systemic diseases affecting the kidney
Manejo de la inmunosupresión en enfermedades sistémicas que afectan al riñón
J. Ballarín, M. Díaz
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        "resumen" => "Hemos revisado la literatura 2007 en relación con 3 grupos de enfermedades sistémicas que afectan al riñón: nefropatía lúpica (NL), vasculitis de pequeño vaso (VPV) y amiloidosis renal. En una revisión sistemática que incluye 268 pacientes con NL reunidos en 4 estudios, el ácido micofenólico (AMF) durante la fase de inducción provoca más remisiones y consigue una mayor supervivencia renal que la ciclofosfamida (CF), en consecuencia se confirma como alternativa válida a la CF. Con un protocolo que incluye rituximab y AMF en la fase de inducción (14 días) el AMF solo, sin corticoides, en la fase de mantenimiento es eficaz y seguro. El rituximab también se ha utilizado con éxito en las formas de NL resistentes a la CF, disminuye la actividad clínica y la proliferación mesangial. Los intercambios plasmáticos consiguen mejores resultados que los bolus de corticoides en las VPV con insuficiencia renal grave. Las complicaciones son severas. Los anti TNFα no aportan beneficio en esta indicación. Los corticoides a dosis bajas, administrados de forma prolongada, disminuyen la incidencia de recidivas. El AMF es una alternativa a la CF en caso de no poderse administrar el fármaco. Con el rituximab se consiguen buenos resultados en las formas resistentes a la CF. Según un ensayo controlado, el tratamiento de la amiloidosis AL con dexametasona y melfalan tiene unos resultados equivalentes a las dosis altas de melfalan y rescate con trasplante con progenitores hematopoyéticos. En la amiloidosis AA, el eprosidate disminuye la velocidad de progresión de la insuficiencia renal."
      ]
      "en" => array:1 [
        "resumen" => "We reviewed the literature in 2007 on 3 groups of systemic diseases affecting the kidney: lupic nephropathy (LN), small vessel vasculitis (SVV) and renal amyloidosis. A systematic review of 268 patients with LN pooled from 4 studies found that mycophenolic acid (MPA) in the induction phase caused more remissions and achieved greater renal survival than cyclophosphamide (CP), confirming it as a valid alternative to CP. Using a protocol including rituximab and MPA in the induction phase (14 days), MPA alone without corticoids is effective and safe in the maintenance phase. Rituximab has also been successfully used in CP-resistant forms of LN, where it reduces clinical activity and mesangial proliferation. Plasma exchanges achieve better results than bolus corticoids in SVS with severe renal failure. Complications are severe. Anti- TNF-α agents provide no benefit in this indication. Prolonged administration of low-dose corticoids reduces the incidence of relapses. MPA is an alternative to CP if this drug cannot be administered. Good results are achieved with rituximab in CP-resistant forms. According to a controlled trial, treatment of AL amyloidosis with dexamethasone and melphalan has equivalent results to highdose melphalan and rescue with hematopoietic stem cell transplant. In AA amyloidosis, eprosidate slows the rate of progression of renal failure."
      ]
    ]
  ]
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  "Apartado" => null
  "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/X2013251408032458?idApp=UINPBA000064"
]
Article information
ISSN: 20132514
Original language: English
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Idiomas
Nefrología (English Edition)